[ Le Syndrome de Kasabach-Merritt: à propos d'un cas ]
Volume 9, Issue 3, November 2014, Pages 1349–1353
Majdouline Boujoual1, Fatima Jabouirik2, Jaouad Kouach3, Driss Moussaoui4, and Mohammed Dehayni5
1 Gynécologie Obstétrique, Hôpital Militaire d’Instruction Mohammed V (HMIMV), Faculté de Médecine et de Pharmacie de Tanger, Université Abdelmalek Essaadi, Morocco
2 Department of Pediatrics, Ibn Sina Hospital Center, Rabat, Morocco
3 Faculté de Médecine et de Pharmacie, Université Mohamed V, Rabat, Morocco
4 Department of Gynecology-Obstetric, Military Training Hospital Med V, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco
5 Department of Gynecology-Obstetric, Military Training Hospital Med V, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco
Original language: French
Copyright © 2014 ISSR Journals. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Kasabach Merritt syndrome is defined by clinical and biological association of a purplish-red vascular tumor rapidly extensive, thrombocytopenia, a variable degree of disseminated intravascular coagulation and sometimes anemia. It usually occurs in neonates and infants less than 6 months, sometimes in utero. The imaging can confirm the diagnosis and search for deep locations. This syndrome can be life-threatening by the risk of bleeding, coagulopathy, thrombosis, compression and heart failure. The therapeutic management should be early, multidisciplinary adapting therapeutic benefits to risks in order to improve the prognosis. We report a case of Kasabach Merritt syndrome, we insist through a literature review of diagnostic, therapeutic and evolutionary difficulties.
Author Keywords: Kasabach Merritt syndrome, physiopathology, diagnosis, complications, treatment.
Volume 9, Issue 3, November 2014, Pages 1349–1353
Majdouline Boujoual1, Fatima Jabouirik2, Jaouad Kouach3, Driss Moussaoui4, and Mohammed Dehayni5
1 Gynécologie Obstétrique, Hôpital Militaire d’Instruction Mohammed V (HMIMV), Faculté de Médecine et de Pharmacie de Tanger, Université Abdelmalek Essaadi, Morocco
2 Department of Pediatrics, Ibn Sina Hospital Center, Rabat, Morocco
3 Faculté de Médecine et de Pharmacie, Université Mohamed V, Rabat, Morocco
4 Department of Gynecology-Obstetric, Military Training Hospital Med V, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco
5 Department of Gynecology-Obstetric, Military Training Hospital Med V, Faculty of Medicine and Pharmacy, Mohammed V University, Rabat, Morocco
Original language: French
Copyright © 2014 ISSR Journals. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
Kasabach Merritt syndrome is defined by clinical and biological association of a purplish-red vascular tumor rapidly extensive, thrombocytopenia, a variable degree of disseminated intravascular coagulation and sometimes anemia. It usually occurs in neonates and infants less than 6 months, sometimes in utero. The imaging can confirm the diagnosis and search for deep locations. This syndrome can be life-threatening by the risk of bleeding, coagulopathy, thrombosis, compression and heart failure. The therapeutic management should be early, multidisciplinary adapting therapeutic benefits to risks in order to improve the prognosis. We report a case of Kasabach Merritt syndrome, we insist through a literature review of diagnostic, therapeutic and evolutionary difficulties.
Author Keywords: Kasabach Merritt syndrome, physiopathology, diagnosis, complications, treatment.
Abstract: (french)
Le syndrome de Kasabach Merritt est un syndrome clinico-biologique défini par l'association d'une tumeur vasculaire rouge-violacée, rapidement extensive, d'une thrombopénie, d'un degré variable de coagulation intra-vasculaire disséminée et parfois d'une anémie. Il survient habituellement chez le nouveau-né et nourrisson de moins de 6 mois, parfois in utero. L'imagerie permet de confirmer le diagnostic et de rechercher des localisations profondes. Ce syndrome peut menacer le pronostic vital par le risque d'hémorragie, coagulopathie, thrombose, compression et défaillance cardiaque. La prise en charge thérapeutique doit être précoce, multidisciplinaire adaptant les bénéfices aux risques thérapeutiques afin d'améliorer le pronostic. Nous rapportons un nouveau cas de syndrome de Kasabach Merritt, nous insisterons à travers une revue de littérature sur les difficultés diagnostiques, thérapeutiques et évolutives.
Author Keywords: Syndrome de Kasabach-Merritt, Physiopathologie, Diagnostic, Complications, Traitement.
How to Cite this Article
Majdouline Boujoual, Fatima Jabouirik, Jaouad Kouach, Driss Moussaoui, and Mohammed Dehayni, “Kasabach-Merritt syndrome: a case report,” International Journal of Innovation and Applied Studies, vol. 9, no. 3, pp. 1349–1353, November 2014.
