Ovarian carcinosarcoma is a rare malignant gynecological tumor that accounts for about 1% of all ovarian cancers. The positive diagnosis of this disease is based on clinical examination, radiological examinations and essentially histological confirmation: the association of a carcinomatous component with a sarcomatous component. Generally, the treatment performed is surgical cytoreduction, followed by chemotherapy and/or radiotherapy. As the prognosis is poor, the survival rate will depend mainly on the quality of surgical management.Multicenter or multinational studies, based on genetic and molecular signaling pathways, are required to better understand this tumor subtype and compare its treatment modalities.