[ Le syndrome de Prune Belly : A propos d’un cas ]
Volume 25, Issue 4, March 2019, Pages 1419–1425
J. Meddah1, F. Abdeddine2, Mounia El Youssfi3, and Samir Bargach4
1 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, Maternité Souissi, Université Mohamed V, Rabat, Morocco
2 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, Maternité Souissi, Université Mohamed V, Rabat, Morocco
3 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, maternité Souissi, Université Mohamed V, Rabat, Morocco
4 Department of Gynecology-Obstetrics-Oncology and High-Risk Pregnancy, Souissi Maternity Hospital, Ibn Sina University Hospital Center, Rabat, Morocco
Original language: French
Copyright © 2019 ISSR Journals. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
The Belly Prune Syndrome is an extremely rare and complex anatomo-radiological entity with a clear male predominance. It is characterized by hypoplasia of the abdominal musculature, abnormalities of the urinary tract and bilateral cryptorchidism forming the classic triad of the syndrome. This pathology is associated in 75% of cases with pulmonary, skeletal, cardiac and gastrointestinal malformations. Nous illustrons l’article par un cas clinique rapportant le diagnostic positif du syndrome de Prune Belly.
Author Keywords: Aplasia of abdominal muscles, bilateral cryptorchidism, urinary malformations, male predominance, antenatal ultrasound, inconstant evolution.
Volume 25, Issue 4, March 2019, Pages 1419–1425
J. Meddah1, F. Abdeddine2, Mounia El Youssfi3, and Samir Bargach4
1 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, Maternité Souissi, Université Mohamed V, Rabat, Morocco
2 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, Maternité Souissi, Université Mohamed V, Rabat, Morocco
3 Service de gynécologie obstétrique cancérologie et grossesse à haut risque, maternité Souissi, Université Mohamed V, Rabat, Morocco
4 Department of Gynecology-Obstetrics-Oncology and High-Risk Pregnancy, Souissi Maternity Hospital, Ibn Sina University Hospital Center, Rabat, Morocco
Original language: French
Copyright © 2019 ISSR Journals. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
The Belly Prune Syndrome is an extremely rare and complex anatomo-radiological entity with a clear male predominance. It is characterized by hypoplasia of the abdominal musculature, abnormalities of the urinary tract and bilateral cryptorchidism forming the classic triad of the syndrome. This pathology is associated in 75% of cases with pulmonary, skeletal, cardiac and gastrointestinal malformations. Nous illustrons l’article par un cas clinique rapportant le diagnostic positif du syndrome de Prune Belly.
Author Keywords: Aplasia of abdominal muscles, bilateral cryptorchidism, urinary malformations, male predominance, antenatal ultrasound, inconstant evolution.
Abstract: (french)
Le syndrome de Prune Belly (SPB) est une entité anatomo-radiologique extrêmement rare et complexe avec une nette prédominance masculine. Il est caractérisé par une hypoplasie de la musculature abdominale, des anomalies du tractus urinaire et une cryptorchidie bilatérale formant la triade classique du syndrome. Cette affection est associée dans 75% des cas à des malformations pulmonaires, squelettiques, cardiaques et gastro-intestinales. Nous illustrons l’article par un cas clinique rapportant le diagnostic positif du syndrome de Prune Belly.
Author Keywords: Aplasie de la musculature abdominale, cryptorchidie bilatérale, malformations urinaires, prédominance masculine, échographie anténatale, évolution variable.
How to Cite this Article
J. Meddah, F. Abdeddine, Mounia El Youssfi, and Samir Bargach, “Prune Belly Syndrome : About a Case,” International Journal of Innovation and Applied Studies, vol. 25, no. 4, pp. 1419–1425, March 2019.
